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Alveolitides, Fibrosing

MedGen UID:
1658997
•Concept ID:
C4721507
•
Disease or Syndrome
Synonyms: Alveolitis, Fibrosing; Fibrosing Alveolitides; Fibrosing Alveolitis; Idiopathic Diffuse Interstitial Pulmonary Fibrosis

Professional guidelines

PubMed

Progressive pulmonary fibrosis: an expert group consensus statement.
Rajan SK, Cottin V, Dhar R, Danoff S, Flaherty KR, Brown KK, Mohan A, Renzoni E, Mohan M, Udwadia Z, Shenoy P, Currow D, Devraj A, Jankharia B, Kulshrestha R, Jones S, Ravaglia C, Quadrelli S, Iyer R, Dhooria S, Kolb M, Wells AU
Eur Respir J 2023 Mar;61(3) Epub 2023 Mar 30 doi: 10.1183/13993003.03187-2021. PMID: 36517177Free PMC Article
Idiopathic Pulmonary Fibrosis (an Update) and Progressive Pulmonary Fibrosis in Adults: An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline.
Raghu G, Remy-Jardin M, Richeldi L, Thomson CC, Inoue Y, Johkoh T, Kreuter M, Lynch DA, Maher TM, Martinez FJ, Molina-Molina M, Myers JL, Nicholson AG, Ryerson CJ, Strek ME, Troy LK, Wijsenbeek M, Mammen MJ, Hossain T, Bissell BD, Herman DD, Hon SM, Kheir F, Khor YH, Macrea M, Antoniou KM, Bouros D, Buendia-Roldan I, Caro F, Crestani B, Ho L, Morisset J, Olson AL, Podolanczuk A, Poletti V, Selman M, Ewing T, Jones S, Knight SL, Ghazipura M, Wilson KC
Am J Respir Crit Care Med 2022 May 1;205(9):e18-e47. doi: 10.1164/rccm.202202-0399ST. PMID: 35486072Free PMC Article
Pulmonary arterial hypertension: pathogenesis and clinical management.
Thenappan T, Ormiston ML, Ryan JJ, Archer SL
BMJ 2018 Mar 14;360:j5492. doi: 10.1136/bmj.j5492. PMID: 29540357Free PMC Article

Recent clinical studies

Etiology

Prognostic value of myositis-specific antibodies in patients with idiopathic interstitial pneumonia.
Wakabayashi H, Iwasaki K, Murakami Y, Takashima K, Kaneko K, Matsuzawa Y
BMC Pulm Med 2024 Oct 10;24(1):503. doi: 10.1186/s12890-024-03326-w. PMID: 39390459Free PMC Article
Identifying prothrombin and bone sialoprotein as potential drug targets for idiopathic pulmonary fibrosis.
Chen Y, Cao S, Shao S, Tong Z
BMC Pulm Med 2024 Oct 7;24(1):488. doi: 10.1186/s12890-024-03289-y. PMID: 39375737Free PMC Article
SCARF2 is a target for chronic obstructive pulmonary disease: Evidence from multi-omics research and cohort validation.
Wang S, Yue Y, Wang X, Tan Y, Zhang Q
Aging Cell 2024 Oct;23(10):e14266. Epub 2024 Jul 3 doi: 10.1111/acel.14266. PMID: 38958042Free PMC Article
Nailfold capillaroscopy findings of interstitial pneumonia with autoimmune features.
Lee SH, Min HK, Kim SH, Kim YW, Yoo KH, Kim HJ, Kim IA, Kim HR
Korean J Intern Med 2023 Nov;38(6):903-911. Epub 2023 Jul 25 doi: 10.3904/kjim.2022.358. PMID: 37488834Free PMC Article
Ineffective esophageal motility is associated with acute rejection after lung transplantation independent of gastroesophageal reflux.
Lo WK, Hiramoto B, Goldberg HJ, Sharma N, Chan WW
World J Gastroenterol 2023 Jun 7;29(21):3292-3301. doi: 10.3748/wjg.v29.i21.3292. PMID: 37377592Free PMC Article

Diagnosis

Treatment patterns and patient journey in progressive pulmonary fibrosis: a cross-sectional survey.
Chaudhuri N, Spagnolo P, Valenzuela C, Amatto VC, Carter OT, Lee L, Small M, Kreuter M
Respir Res 2024 Oct 9;25(1):364. doi: 10.1186/s12931-024-02995-9. PMID: 39385232Free PMC Article
Multicenter study of the performance of NTM Elite agar for the detection of nontuberculous mycobacteria from patients with cystic fibrosis.
André E, Lorent N, Beuselinck K, Deiwick S, Dupont L, Gafsi J, Laenen L, Raymaekers L, Van Bleyenbergh P, Perry JD, Kahl BC
Microbiol Spectr 2024 Oct 3;12(10):e0273623. Epub 2024 Aug 28 doi: 10.1128/spectrum.02736-23. PMID: 39194292Free PMC Article
Evaluation of common protein biomarkers involved in the pathogenesis of respiratory diseases with proteomic methods: A systematic review.
Rezaeeyan H, Arabfard M, Rasouli HR, Shahriary A, Gh BFNM
Immun Inflamm Dis 2023 Nov;11(11):e1090. doi: 10.1002/iid3.1090. PMID: 38018577Free PMC Article
Nailfold capillaroscopy findings of interstitial pneumonia with autoimmune features.
Lee SH, Min HK, Kim SH, Kim YW, Yoo KH, Kim HJ, Kim IA, Kim HR
Korean J Intern Med 2023 Nov;38(6):903-911. Epub 2023 Jul 25 doi: 10.3904/kjim.2022.358. PMID: 37488834Free PMC Article
Ineffective esophageal motility is associated with acute rejection after lung transplantation independent of gastroesophageal reflux.
Lo WK, Hiramoto B, Goldberg HJ, Sharma N, Chan WW
World J Gastroenterol 2023 Jun 7;29(21):3292-3301. doi: 10.3748/wjg.v29.i21.3292. PMID: 37377592Free PMC Article

Therapy

Idiopathic pulmonary fibrosis.
Koudstaal T, Wijsenbeek MS
Presse Med 2023 Sep;52(3):104166. Epub 2023 May 6 doi: 10.1016/j.lpm.2023.104166. PMID: 37156412
Idiopathic pulmonary fibrosis: Current and future treatment.
Glass DS, Grossfeld D, Renna HA, Agarwala P, Spiegler P, DeLeon J, Reiss AB
Clin Respir J 2022 Feb;16(2):84-96. Epub 2022 Jan 10 doi: 10.1111/crj.13466. PMID: 35001525Free PMC Article
Efficacy of antifibrotic drugs, nintedanib and pirfenidone, in treatment of progressive pulmonary fibrosis in both idiopathic pulmonary fibrosis (IPF) and non-IPF: a systematic review and meta-analysis.
Finnerty JP, Ponnuswamy A, Dutta P, Abdelaziz A, Kamil H
BMC Pulm Med 2021 Dec 11;21(1):411. doi: 10.1186/s12890-021-01783-1. PMID: 34895203Free PMC Article
Inflammation and immunity in IPF pathogenesis and treatment.
Heukels P, Moor CC, von der Thüsen JH, Wijsenbeek MS, Kool M
Respir Med 2019 Feb;147:79-91. Epub 2019 Jan 9 doi: 10.1016/j.rmed.2018.12.015. PMID: 30704705
The Bleomycin Model of Pulmonary Fibrosis.
Liu T, De Los Santos FG, Phan SH
Methods Mol Biol 2017;1627:27-42. doi: 10.1007/978-1-4939-7113-8_2. PMID: 28836192

Prognosis

Incidence and prevalence of interstitial lung diseases worldwide: a systematic literature review.
Shah Gupta R, Koteci A, Morgan A, George PM, Quint JK
BMJ Open Respir Res 2023 Jun;10(1) doi: 10.1136/bmjresp-2022-001291. PMID: 37308252Free PMC Article
Efficacy of antifibrotic drugs, nintedanib and pirfenidone, in treatment of progressive pulmonary fibrosis in both idiopathic pulmonary fibrosis (IPF) and non-IPF: a systematic review and meta-analysis.
Finnerty JP, Ponnuswamy A, Dutta P, Abdelaziz A, Kamil H
BMC Pulm Med 2021 Dec 11;21(1):411. doi: 10.1186/s12890-021-01783-1. PMID: 34895203Free PMC Article
Global incidence and prevalence of idiopathic pulmonary fibrosis.
Maher TM, Bendstrup E, Dron L, Langley J, Smith G, Khalid JM, Patel H, Kreuter M
Respir Res 2021 Jul 7;22(1):197. doi: 10.1186/s12931-021-01791-z. PMID: 34233665Free PMC Article
Pulmonary fibrosis, part I: epidemiology, pathogenesis, and diagnosis.
Meyer KC
Expert Rev Respir Med 2017 May;11(5):343-359. Epub 2017 Apr 10 doi: 10.1080/17476348.2017.1312346. PMID: 28345383
Global incidence and mortality of idiopathic pulmonary fibrosis: a systematic review.
Hutchinson J, Fogarty A, Hubbard R, McKeever T
Eur Respir J 2015 Sep;46(3):795-806. Epub 2015 May 14 doi: 10.1183/09031936.00185114. PMID: 25976683

Clinical prediction guides

Sarcoidosis-associated pulmonary fibrosis: joining the dots.
Bandyopadhyay D, Mirsaeidi MS
Eur Respir Rev 2023 Sep 30;32(169) Epub 2023 Sep 27 doi: 10.1183/16000617.0085-2023. PMID: 37758275Free PMC Article
Presentation, diagnosis and clinical course of the spectrum of progressive-fibrosing interstitial lung diseases.
Cottin V, Hirani NA, Hotchkin DL, Nambiar AM, Ogura T, Otaola M, Skowasch D, Park JS, Poonyagariyagorn HK, Wuyts W, Wells AU
Eur Respir Rev 2018 Dec 31;27(150) Epub 2018 Dec 21 doi: 10.1183/16000617.0076-2018. PMID: 30578335Free PMC Article
A multidimensional index and staging system for idiopathic pulmonary fibrosis.
Ley B, Ryerson CJ, Vittinghoff E, Ryu JH, Tomassetti S, Lee JS, Poletti V, Buccioli M, Elicker BM, Jones KD, King TE Jr, Collard HR
Ann Intern Med 2012 May 15;156(10):684-91. doi: 10.7326/0003-4819-156-10-201205150-00004. PMID: 22586007
Pulmonary fibrosis.
Zisman DA, Keane MP, Belperio JA, Strieter RM, Lynch JP 3rd
Methods Mol Med 2005;117:3-44. doi: 10.1385/1-59259-940-0:003. PMID: 16130230Free PMC Article
Mechanisms of pulmonary fibrosis.
Thannickal VJ, Toews GB, White ES, Lynch JP 3rd, Martinez FJ
Annu Rev Med 2004;55:395-417. doi: 10.1146/annurev.med.55.091902.103810. PMID: 14746528

Recent systematic reviews

Incidence and prevalence of interstitial lung diseases worldwide: a systematic literature review.
Shah Gupta R, Koteci A, Morgan A, George PM, Quint JK
BMJ Open Respir Res 2023 Jun;10(1) doi: 10.1136/bmjresp-2022-001291. PMID: 37308252Free PMC Article
Association between genetically determined telomere length and health-related outcomes: A systematic review and meta-analysis of Mendelian randomization studies.
Chen B, Yan Y, Wang H, Xu J
Aging Cell 2023 Jul;22(7):e13874. Epub 2023 May 26 doi: 10.1111/acel.13874. PMID: 37232505Free PMC Article
The Human Respiratory Microbiome: Current Understandings and Future Directions.
Zhao L, Luo JL, Ali MK, Spiekerkoetter E, Nicolls MR
Am J Respir Cell Mol Biol 2023 Mar;68(3):245-255. doi: 10.1165/rcmb.2022-0208TR. PMID: 36476129Free PMC Article
Efficacy of antifibrotic drugs, nintedanib and pirfenidone, in treatment of progressive pulmonary fibrosis in both idiopathic pulmonary fibrosis (IPF) and non-IPF: a systematic review and meta-analysis.
Finnerty JP, Ponnuswamy A, Dutta P, Abdelaziz A, Kamil H
BMC Pulm Med 2021 Dec 11;21(1):411. doi: 10.1186/s12890-021-01783-1. PMID: 34895203Free PMC Article
Pulmonary rehabilitation for interstitial lung disease.
Dowman L, Hill CJ, May A, Holland AE
Cochrane Database Syst Rev 2021 Feb 1;2(2):CD006322. doi: 10.1002/14651858.CD006322.pub4. PMID: 34559419Free PMC Article

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